Presentation of atrial myxoma with unusual clinicopathological features

Sushma HM, Muktha R Pai, Reba Thoppil Philipose

Abstract

Atrial myxomas present with diverse clinical manifestations depending on its location, tendency to embolize, and systemic symptoms resulting from IL-6 production by tumor cells. We present here the case of right atrial myxoma, with persistent anemia and thrombocytopenia. Occurrence of thrombotic episodes with manifestations of antiphospholipid antibody syndrome (APAS) was noted and further investigations were carried out. Transthoracic echocardiogram revealed the presence of a right atrial mass with the possibility of an intracavitary thrombus or myxoma. Complete surgical excision and histopathological examination  further confirmed the diagnosis of right atrial myxoma. The study emphasizes the importance of considering protean clinical manifestations including APAS and histopathological examination while diagnosing right atrial myxoma.


Citation

Sushma HM, Muktha PR, Reba P. IJPLM 2016;2(1):CS3 (Republished: 27 December 2016)

Keywords

Atrial myxoma ; Cardiac tumours; Antiphospholipid syndrome

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