Lupus erythematosus panniculitis presenting with initial periorbital swelling and positive antiphospholipid antibodies: A rare association

Jyotsna Oak, Sama Vasim Rais, Shankar Sawant
DOI: 10.15305/ijrci/v1i1/47

Abstract

Lupus erythematosus panniculitis (LEP), an unusual form of chronic cutaneous lupus erythematosus, is characterized by chronic inflammation and fibrosis of subcutaneous tissue. Clinically, it presents as subcutaneous nodules on common locations such as forehead, cheeks, proximal limbs and buttocks. Ulceration of the nodules may occur in certain cases. Very few case studies have reported the occurrence of early solitary periorbital involvement, highlighting the need for a high index of suspicion in such cases. We report here a case having generalized extensive LEP with initial manifestation of a solitary periorbital swelling, autoimmune hemolytic anemia, and associated antiphospholipid antibodies positivity

Citation

Oak J, Rais S, Sawant S. IJRCI. 2013;1(1):CS6. (4 October 2013)

Keywords

Lupus erythematosus Panniculitis, periorbital, autoimmune hemolytic anemia, antiphospholipid antibodies

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