Rowell syndrome: A case report and review of literature
Keywords:
Rowell syndrome, Lupus erythematosus, Erythema multiformae, Speckled ANAAbstract
Rowell syndrome is a rare disease consisting of lupus erythematosus associated with erythema multiforme-like lesions. The present case study discusses the occurrence of this syndrome in a 38-year-old female who presented with erythematous scaly lesions on face, neck and back, along with the targetoid lesions on upper arms and back of the neck, with oral erosions. Laboratory investigations revealed speckled pattern of anti-nuclear antibody (ANA) with a titer of 1:640, and anti-dsDNA and anti-La (SS-B) positivity. Histology of the targetoid lesion was consistent with erythema multiforme. Significant improvement within four weeks was noted with the use of oral steroids and anti-malarials.
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